Introducción. “Esclerodermia” significa “piel dura”. El término. “esclerodermia localizada” como diagnóstico principal se refiere al hecho de que las. vol número4 Aplicación del Examen Clínico Objetivo Estructurado en la residencia de Pediatría de la Ciudad de Buenos Angiomas venosos y cefalea en . Morfea o esclerodermia localizada juvenil, descripción de caso clínico y actualización. 9. Arkachaisri T, Vilaiyuk S, Li S, O’Neill KM, Pope E, Higgins.
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In juvenile systemic sclerosis JSSca new severity score has been developed and needs to be validated in future trials.
Studies over recent years highlighted the role of imaging as outcome measures for JLS and introduced a severity score for JSSc. The case seclerodermia presented of an 8 year-old girl who presented with indurated hypopigmented plaques, of linear distribution in the right upper extremity of two years onset, together with papery texture hyperpigmented indurated plaques with whitish areas of thinned skin in right lower extremity, and leg and ankle swelling.
The clinical features and diagnostic tests, including histology were compatible with linear and pansclerotic JLS.
New developments have been also reached in the field of outcome measures. Morphea or juvenile localised scleroderma: To report a case of Juvenil Localised scleroderma in esclerodeemia 8-year old girl, contributing to an early diagnosis and treatment.
Morphea or juvenile localised scleroderma JLS is an autoimmune, inflammatory, chronic, slowly progressive connective tissue disease of unknown cause that preferably affects skin and underlying tissues.
Morphea; Juvenile localised scleroderma; Autoimmune.
Esclerodermia: No todo es lupus o artritis en reumatología.
We report a case of linear and pansclerotic ELJ type, in which there was a 2 year delay in diagnosis, however the response to treatment was positive as expected.
She started with immunosuppressive therapy, physiotherapy, and pedistria therapy.
Recent studies, concerning histopathology and clinical associations with other conditions, open new horizons on the etiopathogenesis of scleroderma. Scleroderma, in its localized and systemic presentation, represents the third most frequent esclerodetmia condition in childhood after juvenile idiopathic arthritis and systemic lupus erythematosus. In juvenile localized scleroderma JLSnew techniques such as Doppler and laser Doppler imaging have shown their usefulness for the daily monitoring of the patients.
Early diagnosis, appropriate assessment and effective treatment are crucial to improve the long-term outcome. Finally, a randomized, double-blind controlled trial, a multicenter consensus statement and long-term follow-up studies have confirmed the important role of methotrexate MTX for the treatment of JLS.